These are classification criteria used in research and not necessarily to make the diagnosis in clinical practice.
Contents
Classification criteria Eurofever / PRINO 2019 (Gattorno M, 2019)
Genetic testing shows MEFV genotype and at least one of the following:
- Duration of episode 1-3 days
- Arthritis (joint inflammation)
- Chest pain
- Abdominal pain
OR
Absence of genetic test showing MEFV genotype and at least two of the following:
- Duration of episode 1-3 days
- Arthritis (joint inflammation)
- Chest pain
- Abdominal pain
Suggested criteria (Federci, S, PRINTO / Eurofever 2015)
Occurrence swath
- Episodes <2 days 9
- Chest pain 13
- Abdoninal pain 9
- Ethnicity * 22
- Absence of Oral stomatitis 9
- Absence of Urticarial eczema 15
- Absence of Enlarged throat lymph nodes 10
- Absence of duration of episodes> 6 days 13
TOTAL SCORE at least 60
* Turkish, Armenian, Jewish, Arabic, Italian, Spanish, Greek
Sensitivity: 68%. Specificity: 87%
Livneh A (1997): Criteria: ≥1 major gives sensitivity to 57%, specificity on 99%:
- Major: Attaks with
- Peritonitis
- Pleurisy
- Pericarditis
- MonoArthritis (Hip, knee, ankle)
- Or high fever alone
- Minor: Uncompleted attaks:
- The abdomen (abdominal area)
- Thorax (breast area)
- Joints (Arthritis)
- Bone Pain
- Colchicine-repons
- Supportive: Family incidence, typical ethnicity, <20 years of age first episode, episodes require bed rest, spontaneous remission, asymptomatic intervals. Lab shows inflammation, episodes of ery- / proteinuria, Appendectomy without findings, Parents in the same family
This page has had 1 visits today