
Purple at low platelet count: User Hektor - the English Wikipedia: http://en.wikipedia.org CC BY SA 3.0
Definition
Evans syndrome is Hemolytic anemia + low platelet count (thrombocytopenia), possibly thrombocytopenic purple.
- Evans syndrome can be primary (without associated disease) or secondary to, among other things SLE, Sjøgren`s syndrome, Antifosfolipid syndrome or Hashimoto's thyroiditis.
Disease Cause
Autoimmune disease where antigens attack red blood cells (erythrocytes) and platelets (platelets)
Diagnosis
Blood tests: Detect Hemolytic anemia (high LD, low haptoglobin) and measure low platelet count. Investigate others Autoimmune conditions may be present
Treatment
Corticosteroids, immunoglobulin (IVIG), rarely require additional immunosuppressive treatment (including rituximab).
Literature
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