Similar diseases

• Systemic lupus erythematosus (SLE)
• Systemic JIA in children / Still's disease in (young) adults
• Sepsis
• DRESS syndrome (Drug triggered)
• Kawasaki syndrome (children)

Check if uncertain diagnosis

• Cell countings with differential count of leukocytes
• Blood Cultures
• Coagulation factors (INR, fibrinogen, D-dimer)
• Spinal Fluid
• Viral examinations on
  • EBV
  • CMV
  • Adenovirus
• Bone marrow
• MRI caput
• CT examination cervical
• CT examination thorax
• CT examination abdomen
  • Possibly ultrasound of the abdomen

Complications

Most commonly:

• Pleurisy
• Alveolar hemorrhagia
• Interstitial pneumonitis
• Pericarditis
• Peritoneal acites
• Kidney disorders
• CNS
• DIC
• Uveitis
• Colitis
• Hemophagocytosis (HPS) Most often among children under one year of age

Macrophage activation syndrome, BINDEVEVSSYKDOMMER.no

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