Contents
Definition
Giant cell myocarditis is a rare type of severe heart muscle inflammation for unknown reasons, sometimes related to rheumatic disease.
Occurrence
Concurrent autoimmune disease (connective tissue disorders and others) occur in approximately 20% of cases
Symptoms
Abnormal heart rhythms (Ventricular), heart block, heart attack, heart failure
Diagnosis
Echocardiography, ECG, Cardiac catheter examination with endocardial tissue sample.
- Biopsy: Multinuclear nuclear cells
Treatment
Immunosuppressive treatment can have effect and better survival. Combination of Cyclosporin (Sandimmun) og prednisolone is used. Heart Transplant must be considered.
Literature
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