Scleredema Buschke, Scleredema adultorum 4.67/5 (3)

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Scleredema Buschke (scleredema adultorum of Buschke)

Definition

Sclerotic edema is a rare condition of unknown cause, but often associated with it d diabetes mellitus, Streptococcal infection (In the pharynx) or Monoclonal gammopathy. The skin becomes hard and tight in typical areas of the upper body.

Occurrence

Scleral edema is defined as one rare disease, with closer occurrence is unknown. Most commonly, the disease occurs in middle-aged, obese people with diabetes.

Symptoms

Gradually the skin and subcutaneous tissue become hard, especially over the neck and back. The front of the chest can also be attacked, but usually not arms and legs.

Diagnosis

Disease picture with hard skin, disease history with disease disposition (Diabetes, infection or Monoclonal gammopathy).

Blood tests

  • No special effects. Fasting blood sugar, anti-streptolysin (AST) and electrophoresis to detect any associated diseases. ANA and differential-counting (eosinophilic) leukocytes are examined to assess differential diagnoses (Systemic sclerosis, eosinophilic fasciitis)

Incorrect diagnosis (Similar conditions, differential diagnoses)

Treatment

If there are disabling diseases, these should be treated as well as possible. If significant stiffness, physical therapy may be helpful to counteract more stiffness. Light therapy with UVA1 is being tested in some people.

Medical prognosis

Spontaneous recovery is common, but the condition often lasts for several years. It is unusual that internal organs are attacked

Literature


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